LONG-TERM TEAM DENTAL REHABILITATION OF A YOUNG PATIENT WITH ECTODERMAL DYSPLASIA
Abstract
Today, one of the important issues in dentistry is the treatment of primary adentia, which has its own characteristics, taking into account the age of the patient, the need for orthodontic preparation for prosthetics, the design of the prosthesis. Primary adentia brings not only quantitative changes in the teeth, but also creates conditions for functional and morphological disorders of speech, breathing, chewing, leads to violations of the development of facial skeleton and causes underdevelopment of the jaws, which reduces the quality of life of the patient. Primary adentia with multiple missing teeth is a genetically determined condition and very often has a hereditary character in the form of hypohidrotic and hydrotic dysplasia. We present to your attention a description of the complex work of dentists on the completed case of a patient with a diagnosis of hypohidrotic ectodermal dysplasia (Christ-Siemens-Touraine syndrome). With multiple adentia, it is necessary to provide denture care as soon as possible, which requires engagement of dentists of various specialties in treatment and rehabilitation: orthodontists, orthopedists, therapists and maxillofacial surgeons
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