COMBINATION OF TETRALOGY OF FALLOT AND HEMOPHILIA IN A CHILD: CASE REPORT

Kulikova D. O.; Pisklova Y. V.; Buchnieva O. V.; Piddubna I. M.

doi:10.31435/rsglobal_ws/31072019/6588

Kulikova D. O. Dr., ST “Zaycev V.T. Institute of General and Urgent Surgery AMS of Ukraine”, Kharkiv
Pisklova Y. V. Dr., ST “Zaycev V.T. Institute of General and Urgent Surgery AMS of Ukraine”, Kharkiv
Buchnieva O. V. PhD, ST “Zaycev V.T. Institute of General and Urgent Surgery AMS of Ukraine”, Kharkiv
Piddubna I. M. PhD, Department of Pediatrics No2, Kharkiv National Medical University, Ukraine

DOI: https://doi.org/10.31435/rsglobal_ws/31072019/6588

Keywords: congenital heart disease, tetralogy of Fallot, hemophilia A, surgical treatment, coagulopathy

Abstract

Congenital heart disease (CHD) is formed during intrauterine period but, as a rule, they are not hereditary. Hemophilia A belongs to the group of hereditary coagulopathies stipulated by deficiency of coagulation factor VIII and characterized by bleeding of hematoma like type. Combination of these two diseases is rather rare that requires cardiosurgeons’ apprehensive attitude.
We present our experience in surgical treatment of a boy of 8 months old with Tetralogy of Fallot. Hemophilia A was found in preoperative examination. He was successfully operated with cardiac pulmonary bypass on the background of factor VII injection.
Surgical treatment was successful without significant bleeding. Postoperative period was uneventful. For successful treatment of CHD with coagulation failure is very important timely diagnosis, that can be difficult due to the lack of specific symptoms in children.
Surgical treatment is the method of choice in TOF. Timely and complete diagnosis of comorbidities allows to make it safe even in case of Hemophilia A.

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